Pathways Knowlegdes

Biological pathway database


Pathway DOIs Note
3-Methylcrotonyl-CoA Carboxylase Deficiency Type I

Accession ID: PathBank:SMP0120662
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3-Hydroxyisobutyric Aciduria

Accession ID: PathBank:SMP0120806
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3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency

Accession ID: PathBank:SMP0120440
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3-Methylglutaconic Aciduria Type IV

Accession ID: PathBank:SMP0120444
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Maple Syrup Urine Disease

Accession ID: PathBank:SMP0120516
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Isovaleric Acidemia

Accession ID: PathBank:SMP0120589
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Secondary Metabolites: Leucine Biosynthesis

Accession ID: PathBank:SMP0121332
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Valine, Leucine, and Isoleucine Degradation

Accession ID: PathBank:SMP0000032
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beta-Ketothiolase Deficiency

Accession ID: PathBank:SMP0000173
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Maple Syrup Urine Disease

Accession ID: PathBank:SMP0000199
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Methylmalonate Semialdehyde Dehydrogenase Deficiency

Accession ID: PathBank:SMP0000384
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3-Methylglutaconic Aciduria Type IV

Accession ID: PathBank:SMP0000141
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Isovaleric Acidemia

Accession ID: PathBank:SMP0000524
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Leucine Degradation

Accession ID: PathBank:SMP0002433
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Valine, Leucine, and Isoleucine Degradation

Accession ID: PathBank:SMP0087234
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3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency

Accession ID: PathBank:SMP0120661
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3-Methylglutaconic Aciduria Type IV

Accession ID: PathBank:SMP0120665
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Methylmalonic Aciduria

Accession ID: PathBank:SMP0120745
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Propionic Acidemia

Accession ID: PathBank:SMP0120757
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3-Hydroxyisobutyric Acid Dehydrogenase Deficiency

Accession ID: PathBank:SMP0120805
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