BioCyc:OHMETHYLBILANESYN-RXN
This reaction formsthe first tetrapyrrole compound. In the presence of a secondenzyme, EC 4.2.1.75 (uroporphyrinogen-III synthase), often calledco-synthase, the product is cyclized to form uroporphyrinogen-III.
WATER + 4 PORPHOBILINOGEN --> 4 AMMONIUM + HYDROXYMETHYLBILANE
H2O[H2O] + 4 Porphobilinogen[C10H14N2O4] = 4 NH4+[NH4] + Hydroxymethylbilane[C40H46N4O17]
DB Links
- BioCyc: OHMETHYLBILANESYN-RXN
- EC Number: 2.5.1.61
Alias
Metabolites
Substrates
| metabolite | compartment | Structure |
|---|---|---|
| H2O Formula: H2O |
Cytoplasm | |
| Porphobilinogen Formula: C10H14N2O4 |
Cytoplasm |
Products
| metabolite | compartment | Structure |
|---|---|---|
| NH4+ Formula: NH4 |
Cytoplasm | |
| Hydroxymethylbilane Formula: C40H46N4O17 |
Cytoplasm |