Pathways Knowlegdes

Biological pathway database


Pathway DOIs Note
Isobutyryl-CoA Dehydrogenase Deficiency

Accession ID: PathBank:SMP0120588
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tRNA Charging 2

Accession ID: PathBank:SMP0121283
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3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency

Accession ID: PathBank:SMP0000138
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3-Methylglutaconic Aciduria Type III

Accession ID: PathBank:SMP0000140
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Isovaleric Aciduria

Accession ID: PathBank:SMP0000238
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Isobutyryl-CoA Dehydrogenase Deficiency

Accession ID: PathBank:SMP0000523
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Isoleucine Degradation

Accession ID: PathBank:SMP0002390
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Valine, Leucine, and Isoleucine Degradation

Accession ID: PathBank:SMP0063689
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2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency

Accession ID: PathBank:SMP0120660
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3-Methylglutaconic Aciduria Type III

Accession ID: PathBank:SMP0120664
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Maple Syrup Urine Disease

Accession ID: PathBank:SMP0120736
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Isovaleric Acidemia

Accession ID: PathBank:SMP0120808
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3-Methylcrotonyl-CoA Carboxylase Deficiency Type I

Accession ID: PathBank:SMP0120441
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Methylmalonic Aciduria

Accession ID: PathBank:SMP0120525
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Propionic Acidemia

Accession ID: PathBank:SMP0120537
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3-Hydroxyisobutyric Acid Dehydrogenase Deficiency

Accession ID: PathBank:SMP0120586
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tRNA Charging

Accession ID: PathBank:SMP0121281
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Isoleucine Biosynthesis

Accession ID: PathBank:SMP0121293
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2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency

Accession ID: PathBank:SMP0000137
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3-Methylcrotonyl-CoA Carboxylase Deficiency Type I

Accession ID: PathBank:SMP0000237
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