EC: 4.4.1.2

homocysteine desulfhydrase (L-homocysteine hydrogen-sulfide-lyase (deaminating; 2-oxobutanoate-forming))

enzyme lambda metabolic reaction experiment

Pathways

pathway id name
BioCyc:META_PWY-5328 superpathway of L-methionine salvage and degradation
BioCyc:META_PWY66-426 hydrogen sulfide biosynthesis II (mammalian)
BioCyc:MOUSE_PWY-5328 superpathway of methionine degradation
BioCyc:MOUSE_PWY-6292 cysteine biosynthesis III (mammalia)
BioCyc:HUMAN_PWY66-426 hydrogen sulfide biosynthesis II (mammalian)
BioCyc:META_PWY-6292 superpathway of L-cysteine biosynthesis (mammalian)
BioCyc:MOUSE_HOMOCYSDEGR-PWY cysteine biosynthesis/homocysteine degradation
BioCyc:META_HOMOCYSDEGR-PWY L-cysteine biosynthesis III (from L-homocysteine)
BioCyc:META_PWY-701 L-methionine degradation II
BioCyc:MOUSE_CYSTEINE-SYN2-PWY cysteine biosynthesis II
Reactome:R-HSA-1614558 Degradation of cysteine and homocysteine
Reactome:R-MMU-1430728 Metabolism
Reactome:R-MMU-1614558 Degradation of cysteine and homocysteine
Reactome:R-RNO-1614558 Degradation of cysteine and homocysteine
Reactome:R-DDI-71291 Amino acid and derivative metabolism
Reactome:R-DDI-1614558 Degradation of cysteine and homocysteine
Reactome:R-HSA-1614603 Cysteine formation from homocysteine
Reactome:R-HSA-2408508 Metabolism of ingested SeMet, Sec, MeSec into H2Se
Reactome:R-MMU-1614603 Cysteine formation from homocysteine
Reactome:R-RNO-1614603 Cysteine formation from homocysteine
Reactome:R-DDI-1614635 Sulfur amino acid metabolism
Reactome:R-HSA-71291 Amino acid and derivative metabolism
Reactome:R-MMU-71291 Amino acid and derivative metabolism
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-71291 Amino acid and derivative metabolism
Reactome:R-DDI-1430728 Metabolism
Reactome:R-DDI-1614603 Cysteine formation from homocysteine
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-1614635 Sulfur amino acid metabolism
Reactome:R-HSA-2408522 Selenoamino acid metabolism
Reactome:R-MMU-1614635 Sulfur amino acid metabolism
Reactome:R-RNO-1614635 Sulfur amino acid metabolism
WikiPathways:WP5355 Metabolic Epileptic Disorders
WikiPathways:WP4504 Cysteine and methionine catabolism
PathBank:SMP0120654 Cystinosis, Ocular Nonnephropathic
PathBank:SMP0120694 Dihydropyrimidine Dehydrogenase Deficiency (DHPD)
PathBank:SMP0120718 Hypermethioninemia
PathBank:SMP0120754 Non-Ketotic Hyperglycinemia
PathBank:SMP0120770 Hyperglycinemia, Non-Ketotic
PathBank:SMP0120798 gamma-Cystathionase Deficiency (CTH)
PathBank:SMP0000177 Cystathionine beta-Synthase Deficiency
PathBank:SMP0000340 Methylenetetrahydrofolate Reductase Deficiency (MTHFRD)
PathBank:SMP0000242 Dimethylglycine Dehydrogenase Deficiency
PathBank:SMP0000223 Non-Ketotic Hyperglycinemia
PathBank:SMP0000484 Dimethylglycine Dehydrogenase Deficiency
PathBank:SMP0000722 Cystinosis, Ocular Nonnephropathic
PathBank:SMP0087290 Cysteine Metabolism
PathBank:SMP0087298 Homocysteine Degradation
PathBank:SMP0087338 Glycine and Serine Metabolism
PathBank:SMP0087342 Methionine Metabolism
PathBank:SMP0120653 3-Phosphoglycerate Dehydrogenase Deficiency
PathBank:SMP0120741 Sarcosinemia
PathBank:SMP0120853 Homocystinuria-Megaloblastic Anemia Due to Defect in Cobalamin Metabolism, cblG Complementation Type
PathBank:SMP0120873 Cystinosis, Ocular Nonnephropathic
PathBank:SMP0120471 Cystathionine beta-Synthase Deficiency
PathBank:SMP0120475 Dimethylglycine Dehydrogenase Deficiency
PathBank:SMP0120487 Glycine N-Methyltransferase Deficiency
PathBank:SMP0120519 Methionine Adenosyltransferase Deficiency
PathBank:SMP0120527 S-Adenosylhomocysteine (SAH) Hydrolase Deficiency
PathBank:SMP0120564 beta-Mercaptolactate-Cysteine Disulfiduria
PathBank:SMP0120580 Homocystinuria, Cystathionine beta-Synthase Deficiency
PathBank:SMP0000004 Glycine and Serine Metabolism
PathBank:SMP0000033 Methionine Metabolism
PathBank:SMP0000455 Homocysteine Degradation
PathBank:SMP0000222 Glycine N-Methyltransferase Deficiency
PathBank:SMP0000499 beta-Mercaptolactate-Cysteine Disulfiduria
PathBank:SMP0000515 Homocystinuria, Cystathionine beta-Synthase Deficiency
PathBank:SMP0000721 3-Phosphoglycerate Dehydrogenase Deficiency
PathBank:SMP0087273 Selenoamino Acid Metabolism
PathBank:SMP0063587 Selenoamino Acid Metabolism
PathBank:SMP0063607 Cysteine Metabolism
PathBank:SMP0063637 Methionine Metabolism
PathBank:SMP0120872 3-Phosphoglycerate Dehydrogenase Deficiency
PathBank:SMP0120521 Sarcosinemia
PathBank:SMP0120634 Homocystinuria-Megaloblastic Anemia Due to Defect in Cobalamin Metabolism, cblG Complementation Type
PathBank:SMP0000013 Cysteine Metabolism
PathBank:SMP0000341 Hypermethioninemia
PathBank:SMP0000221 Methionine Adenosyltransferase Deficiency
PathBank:SMP0000179 Dihydropyrimidine Dehydrogenase Deficiency (DHPD)
PathBank:SMP0000485 Hyperglycinemia, Non-Ketotic
PathBank:SMP0063628 Homocysteine Degradation
PathBank:SMP0120691 Cystathionine beta-Synthase Deficiency
PathBank:SMP0120695 Dimethylglycine Dehydrogenase Deficiency
PathBank:SMP0120707 Glycine N-Methyltransferase Deficiency
PathBank:SMP0120739 Methionine Adenosyltransferase Deficiency
PathBank:SMP0120747 S-Adenosylhomocysteine (SAH) Hydrolase Deficiency
PathBank:SMP0120783 beta-Mercaptolactate-Cysteine Disulfiduria
PathBank:SMP0120799 Homocystinuria, Cystathionine beta-Synthase Deficiency
PathBank:SMP0120474 Dihydropyrimidine Dehydrogenase Deficiency (DHPD)
PathBank:SMP0120498 Hypermethioninemia
PathBank:SMP0120534 Non-Ketotic Hyperglycinemia
PathBank:SMP0120550 Hyperglycinemia, Non-Ketotic
PathBank:SMP0120579 gamma-Cystathionase Deficiency (CTH)
PathBank:SMP0000029 Selenoamino Acid Metabolism
PathBank:SMP0000214 S-Adenosylhomocysteine (SAH) Hydrolase Deficiency
PathBank:SMP0000244 Sarcosinemia
PathBank:SMP0000514 gamma-Cystathionase Deficiency (CTH)
PathBank:SMP0000570 Homocystinuria-Megaloblastic Anemia Due to Defect in Cobalamin Metabolism, cblG Complementation Type
PathBank:SMP0063626 Glycine and Serine Metabolism