Mitochondrion nucleoid
The mitochondrial nucleoid is the specialized, non-membrane-bound region within the mitochondrial matrix where mitochondrial DNA (mtDNA) is organized and maintained. It associates mtDNA with proteins (e.g., TFAM) to facilitate replication, transcription, and segregation, ensuring proper mitochondrial genome function and inheritance—distinct from nuclear genomic organization.
Metabolites
Proteins
KGD1;
KGD1;
CLPX;
MPG;
SHMT2;
POLG;
TFAM;
SSBP1;
MTERF2;
TRMT10C;
DHX30;
FASTKD5;
SUPV3L1;
TEFM;
TWNK;
HSD17B10;
ELAC2;
UQCC2;
MTNAP1;
DDX28;
ATAD3A;
FASTKD2;
POLG2;
ELAC2;
POLG;
POLG;
A8K5G6_HUMAN;
B3KSU9_HUMAN;
B3KT00_HUMAN;
B4DT15_HUMAN;
B4E365_HUMAN;
POLG;
E5KNV8_HUMAN;
E5KNW2_HUMAN;
E5KNX5_HUMAN;
POLG2;
TFAM;
E5KSY5_HUMAN;
ELAC2;
ELAC2;
POLG;
DHX30;
C10orf2;
ELAC2;
SSBP1;
POLG;
POLG;
SSBP1;
SSBP1;
SSBP1;
E5KS22_HUMAN;
E5KSX8_HUMAN;
SSBP1;
TFAM;
SSBP1;
UQCC2;
TFAM;
UQCC2;
CLPX;
MPG;
SHMT2;
POLG;
TFAM;
SSBP1;
MTERF2;
TRMT10C;
DHX30;
FASTKD5;
SUPV3L1;
TEFM;
TWNK;
HSD17B10;
ELAC2;
UQCC2;
MTNAP1;
DDX28;
ATAD3A;
FASTKD2;
POLG2;
ELAC2;
POLG;
POLG;
A8K5G6_HUMAN;
B3KSU9_HUMAN;
B3KT00_HUMAN;
B4DT15_HUMAN;
B4E365_HUMAN;
POLG;
E5KNV8_HUMAN;
E5KNW2_HUMAN;
E5KNX5_HUMAN;
POLG2;
TFAM;
E5KSY5_HUMAN;
ELAC2;
ELAC2;
POLG;
DHX30;
C10orf2;
ELAC2;
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